A Literature Review on Arnold-Chiari Disease in Children (Evaluation of Surgical Approach and Post-Surgical Management)

Authors

  • Michael Department of Neurosurgery, Faculty of Medicine, Universitas Padjadjaran, Sumedang, 45363, Indonesia
  • Rully Hanafi Dahlan Department of Neurosurgery, Faculty of Medicine, Universitas Padjadjaran, Sumedang, 45363, Indonesia
  • Sevline Estethia Ompusunggu Department of Neurosurgery, Faculty of Medicine, Universitas Padjadjaran, Sumedang, 45363, Indonesia

DOI:

https://doi.org/10.32734/sumej.v8i1.16431

Keywords:

arnold-chiari disease, children, posterior decompression surgery, post-surgical management

Abstract

Background: Arnold-Chiari (AC) disease in children is a complex congenital condition requiring multidisciplinary management. Surgical intervention is often necessary to correct affected anatomy and alleviate symptoms. Objective: To investigate surgical approaches and post-surgical management of AC in children and identify knowledge gaps. Methods: Literature search was systematically conducted through PubMed using relevant keywords. Inclusion criteria encompassed studies within the past 15 years pertaining to pediatric neurosurgery and Chiari. Results: Six relevant studies highlighted the importance of intraoperative electrophysiological monitoring, comparison of outcomes between posterior decompression with and without duraplasty, correlation of CSF flow with surgical outcomes, post-operative pain management, and indications for syringosubarachnoid shunt placement. Knowledge gaps remain regarding long-term effects of monitoring techniques, surgical outcome comparisons, CSF flow relationships, and pain management. Conclusion: Surgical intervention for AC in children is critical, yet meticulous post-surgical management is required. Cross-disciplinary collaboration and a holistic approach are necessary to enhance understanding and care of AC in children.

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Published

2025-01-01

How to Cite

1.
Michael, Hanafi Dahlan R, Estethia Ompusunggu S. A Literature Review on Arnold-Chiari Disease in Children (Evaluation of Surgical Approach and Post-Surgical Management). Sumat. Med. J. [Internet]. 2025Jan.1 [cited 2025Aug.4];8(1):53-67. Available from: https://idjpcr.usu.ac.id/smj/article/view/16431

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Section

Systematic Review and Meta-Analysis